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左冠状动脉开口处闭锁及瓣上主动脉狭窄的外科治疗

Surgical management of left coronary artery ostial atresia and supravalvar aortic stenosis.

作者信息

Rosenkranz E R, Murphy D J, Cosgrove D M

机构信息

Department of Thoracic and Cardiovascular Surgery, Cleveland Clinic Foundation, Ohio 44195-5066.

出版信息

Ann Thorac Surg. 1992 Oct;54(4):779-81. doi: 10.1016/0003-4975(92)91031-4.

DOI:10.1016/0003-4975(92)91031-4
PMID:1417243
Abstract

Congenital atresia of the left main coronary artery ostium is a rare lesion, particularly when found in association with supravalvar aortic stenosis. This report describes the preoperative evaluation and surgical management of this lesion found in conjunction with a quadricuspid aortic valve in a 5-year-old child. Patch aortoplasty and left internal thoracic artery to left anterior descending coronary artery bypass were performed to correct this lesion.

摘要

先天性左冠状动脉主干口闭锁是一种罕见的病变,尤其是当它与主动脉瓣上狭窄同时存在时。本报告描述了一名5岁儿童同时合并四叶式主动脉瓣时,对此病变的术前评估和手术处理。采用补片主动脉成形术和左胸廓内动脉至左前降支冠状动脉搭桥术来矫正此病变。

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