Furihata A, Sasaki Y, Furihata Y, Koike S, Takayama S, Furuta S
Second Department of Internal Medicine, Shinshu University School of Medicine.
Kokyu To Junkan. 1992 Nov;40(11):1139-42.
A 19 year-old girl with an unusual type of coarctation of the aorta terminating in complete obstruction is presented. At the age of 5 years, she was diagnosed by aortography to have coarctation of the aorta of type IV C according to Edward's classification. No surgical treatment was performed at that time because her growth was good and she didn't have hypertension. During the follow-up period, marked hypertension developed, and she was readmitted. The aortogram revealed a bicuspid aortic valve and total obstruction of the descending thoracic aorta at the site where coarctation was noticed previously. The abdominal aorta distal from the obstruction site was filled through rich collateral circulation. As these angiographic interval changes are very rare, we discussed the genesis of obstruction and operative indication by reviewing the literature.
本文报告了一名19岁女孩,患有罕见类型的主动脉缩窄,最终导致完全梗阻。5岁时,经主动脉造影检查,根据爱德华兹分类法诊断为IV C型主动脉缩窄。当时未进行手术治疗,因为她生长发育良好且无高血压。在随访期间,她出现了明显的高血压,因此再次入院。主动脉造影显示为二叶式主动脉瓣,降主动脉在先前发现缩窄的部位完全梗阻。梗阻部位远端的腹主动脉通过丰富的侧支循环供血。由于这些血管造影的间隔期变化非常罕见,我们通过回顾文献讨论了梗阻的发生机制和手术指征。