施皮勒梅耶-沃格特-巴滕病中红细胞的硫辛酰脱氢酶活性
Lipoyl dehydrogenase activity of erythrocytes in Spielmeyer-Vogt-Batten's disease.
作者信息
Plum C M
出版信息
Acta Med Okayama. 1977 Aug;31(4):249-55.
PMID:145161
Abstract
Using the method for the determination of the lipoyl dehydrogenase activity in intact erythrocytes described by Seet and Lee (1975), it was demonstrated that in patients with Spielmeyer-Vogt-Batten's disease, this activity was around the lower limit of normal. In these patients, the enzymatic activity is significantly reduced to such an extent that it may affect the function and metabolism of the erythrocytes.
摘要
采用Seet和Lee（1975年）所描述的完整红细胞中硫辛酰脱氢酶活性的测定方法，结果表明，在患有施皮尔曼-沃格特-巴滕病的患者中，这种活性约为正常下限。在这些患者中，酶活性显著降低，以至于可能影响红细胞的功能和代谢。
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