[非淀粉样轻链沉积性心肌病中的外周栓塞]

[Peripheral embolism in nonamyloidotic light-chain deposition cardiomyopathy].

作者信息

Saura Daniel, Bixquert David, Montoya José J, Soria Federico, Bas Agueda, Valdés Mariano

机构信息

Servicio de Cardiología. Hospital Virgen de la Arrixaca. Murcia. Spain.

出版信息

Rev Esp Cardiol. 2003 Sep;56(9):921-2. doi: 10.1016/s0300-8932(03)76982-6.

DOI:10.1016/s0300-8932(03)76982-6

PMID:14519281

Abstract

Nonamyloidotic light-chain cardiomyopathy is a paraproteinemia-induced disorder. Unlike amyloidosis, light chain deposition may be reversible with appropriate treatment. We report a case of fatal light chain deposition disease manifested as cardiomyopathy, which was complicated by arterial embolism despite the maintenance of sinus rhythm.

摘要

非淀粉样轻链心肌病是一种由副蛋白血症引起的疾病。与淀粉样变性不同，轻链沉积在适当治疗下可能是可逆的。我们报告一例致命的轻链沉积病，表现为心肌病，尽管维持窦性心律仍并发动脉栓塞。