[Neurofibromatosis of the head and neck].

The source of development of neurofibromas, their incidence, tendency for recurrences and malignant transformation are reviewed. The main signs of von Recklinghausen disease and the difficulties in its diagnosis are discussed. A case of faciocervical neurofibromatosis with recurrences is presented stressing the importance of adequate therapeutic-prophylactic management is stressed, in view of increased predisposition to recurrences and malignant transformation.