Lam Chung-Wah, Kuo Shou-Jen, Chang Hung-Chi, Chen Shou-Tong, Chen Yao-Li, Yang Li-Heng, Hsieh Ching-Shui
Department of General Surgery, Changhua Christian Hospital, Changhua, Taiwan, ROC.
Int Surg. 2003 Jul-Sep;88(3):133-6.
This report demonstrates the cases of a 47-year-old housewife, a 54-year-old female, and an 80-year-old woman in whom pseudomyxoma peritonei was found accidentally during surgery. Pseudomyxoma peritonei is a rare disease. No effective treatment is known. Modern treatments include radical surgical excision with appendicectomy and oophorectomy in women and adjuvant hyperthermic intraperitoneal and systemic chemotherapy. Major causes of morbidity and mortality are bowel obstruction and biliary obstruction. Five-year survival rate, depending on whether the disease is benign or malignant, is about 53-75%. Median survival is about 2 years under surgical management.
本报告展示了一名47岁家庭主妇、一名54岁女性和一名80岁女性的病例,她们在手术过程中意外发现患有腹膜假黏液瘤。腹膜假黏液瘤是一种罕见疾病。目前尚无已知的有效治疗方法。现代治疗方法包括在女性患者中进行根治性手术切除并附加阑尾切除术和卵巢切除术,以及辅助性热灌注腹腔化疗和全身化疗。发病和死亡的主要原因是肠梗阻和胆管梗阻。根据疾病是良性还是恶性,五年生存率约为53%-75%。在手术治疗下,中位生存期约为2年。