Hofman Véronique, Venissac Nicolas, Mouroux Jérôme, Dugue Pierre, Hofman Paul
Service d'Anatomie Pathologique, Hôpital Pasteur, 06002 Nice Cedex 01.
Ann Pathol. 2003 Sep;23(4):332-5.
Primitive intrathoracic liposarcomas are rare tumors mostly located in the mediastinum or in lung parenchyma. Primitive liposarcomas of the pleura are exceptional and show a dramatic clinical course. These tumors are treated by surgery sometimes associated with radiotherapy. We report 2 cases of primitive liposarcoma of the pleura occurring in 2 women of 19 and 62 years of age. Histological examination showed in both cases a low-grade myxoid liposarcoma. In one case, ultrastructural study confirmed the diagnosis.
原发性胸内脂肪肉瘤是罕见肿瘤,大多位于纵隔或肺实质。胸膜原发性脂肪肉瘤极为罕见,临床病程凶险。这些肿瘤有时采用手术联合放疗进行治疗。我们报告2例胸膜原发性脂肪肉瘤,分别发生于19岁和62岁的女性。组织学检查在两例中均显示为低级别黏液样脂肪肉瘤。其中1例经超微结构研究确诊。