Xiong Wei-ning, Fang Hui-juan, Xu Yong-jian, Xiong Sheng-dao, Zhang Hui-lan, Zuo Peng
Department of Respiratory Medicine, Tongji Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan 430030, China.
Zhonghua Jie He He Hu Xi Za Zhi. 2007 May;30(5):352-4.
Primary liposarcoma of the pleura is extremely rare. The first case report in China was described.
The clinical data of a case of primary liposarcoma of the pleura diagnosed in this hospital were reported, and the pertinent literature was reviewed.
A total of 17 cases of primary liposarcomas of the pleura, including the case reported herein, had been described in international literature. Primary pleural liposarcomas occur predominantly in males and older patients, and the myxoid histological subtype is common. The most common symptoms are chest pain and shortness of breath. Radiographic and surgical evaluation are important for its diagnosis. Surgical resection with adjuvant radiation therapy is recommended for the disease.
More data are required for the treatment and prognostic evaluation of the primary liposarcoma of the pleura.
胸膜原发性脂肪肉瘤极为罕见。本文报道了中国首例病例。
报告本院诊断的1例胸膜原发性脂肪肉瘤的临床资料,并复习相关文献。
国际文献中已描述了包括本文报道病例在内的共17例胸膜原发性脂肪肉瘤。原发性胸膜脂肪肉瘤主要发生于男性及老年患者,黏液样组织学亚型常见。最常见的症状是胸痛和气短。影像学和手术评估对其诊断很重要。推荐对该病行手术切除并辅以放射治疗。
胸膜原发性脂肪肉瘤的治疗和预后评估需要更多数据。