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法洛四联症合并肺动脉闭锁时主主动脉-肺动脉侧支动脉的产前表现。

Prenatal demonstration of major aortopulmonary collateral arteries with tetralogy of Fallot and pulmonary atresia.

作者信息

Miyashita Susumu, Chiba Yoshihide

机构信息

Department of Perinatology, National Cardiovascular Center, Osaka, Japan.

出版信息

Fetal Diagn Ther. 2004 Jan-Feb;19(1):100-5. doi: 10.1159/000074270.

DOI:10.1159/000074270
PMID:14646428
Abstract

Major aortopulmonary collateral arteries were prenatally demonstrated in a case of tetralogy of Fallot and pulmonary atresia (TOF-PA). Color Doppler and pulsed Doppler ultrasonography revealed abnormal arteries arising directly from the descending aorta. An aortogram after birth confirmed two collateral arteries arising from the descending aorta and one from the left subclavian artery. Fetal echocardiography was essential for the diagnosis of TOF-PA, but further examination was needed to find collateral arteries, which provided useful information for management after birth.

摘要

在一例法洛四联症合并肺动脉闭锁(TOF-PA)病例中,产前显示出主要的体肺侧支动脉。彩色多普勒和脉冲多普勒超声检查显示异常动脉直接发自降主动脉。出生后的主动脉造影证实有两条侧支动脉发自降主动脉,一条发自左锁骨下动脉。胎儿超声心动图对TOF-PA的诊断至关重要,但需要进一步检查以发现侧支动脉,这为出生后的治疗提供了有用信息。

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