Rabii Redouane, el Mejjad Amine, Fekak Hamid, Querfani Baderdine, Joual Abdenbi, el Mrini Mohamed
Service d'Urologie A, CHU Ibn Rochd, Casablanca, Maroc.
Prog Urol. 2003 Sep;13(4):686-9.
Upper urinary tract tumours are exceptional in the context of renal polycystic disease. The authors report the case of Mrs B. F., 56 years old, who presented with left loin pain associated with haematuria. Clinical examination was normal and ultrasound examination revealed bilateral renal polycystic disease with a mass in the left renal sinus. CT urography showed a tumour arising from the renal pelvis suggestive of an upper urinary tract tumour. The laboratory assessment revealed normal renal function and normal urine cytology. Treatment consisted of radical nephroureterectomy with resection of a bladder cuff. Histological examination revealed a urothelial tumour of the renal pelvis with negative surgical margins. In the light of this case, the authors discuss the diagnostic difficulties and specificities, the treatment and the outcome of this unusual clinical association.
在上尿路肿瘤合并肾多囊性疾病的情况下，此类病例较为罕见。作者报告了56岁的B.F.女士的病例，她出现左侧腰痛并伴有血尿。临床检查正常，超声检查显示双侧肾多囊性疾病，左侧肾窦有一肿块。CT尿路造影显示肾盂有一肿瘤，提示为上尿路肿瘤。实验室评估显示肾功能正常，尿细胞学检查正常。治疗包括根治性肾输尿管切除术及膀胱袖口切除术。组织学检查显示肾盂尿路上皮肿瘤，手术切缘阴性。鉴于此病例，作者讨论了这种不寻常临床关联的诊断困难与特点、治疗方法及预后情况。
