Shiba Masahiro, Takatera Hiroshi
Urologic Clinic, Yao Tokusyukai General Hospital.
Hinyokika Kiyo. 2003 Oct;49(10):611-3.
We report a very rare case of retroperitoneal angiomyolipoma with rapidly progressing intracytic hemorrhage and lymph node involvement in a 34-year-old female. She was admitted to our hospital complaining of a severe pain in the lower abdominal region, followed by oligemic shock. Abdominal enhanced computed tomography (CT) demonstrated a retroperitoneal giant cyst with intracystic hematoma, which displaced the left kidney anteriorly. Because transarterial embolization was unsuccessful transabdominal left nephrectomy combined with excision of the giant cyst was performed to keep the continuing hemorrhage under control. Simultaneously, a swollen paraaortic lymph node was also resected. The histologic findings of resected tissue and lymph node were retroperitoneal angiomyolipoma with lymph node involvement. The patient is being followed up at our hospital without recurrence.
我们报告了一例非常罕见的腹膜后血管平滑肌脂肪瘤病例，该病例发生于一名34岁女性，伴有迅速进展的细胞内出血和淋巴结受累。她因下腹部剧痛入院，随后出现低血容量性休克。腹部增强计算机断层扫描（CT）显示一个伴有囊内血肿的腹膜后巨大囊肿，该囊肿将左肾向前推移。由于经动脉栓塞术未成功，遂行经腹左肾切除术并切除巨大囊肿以控制持续出血。同时，还切除了一个肿大的主动脉旁淋巴结。切除组织和淋巴结的组织学检查结果为腹膜后血管平滑肌脂肪瘤伴淋巴结受累。该患者正在我院接受随访，未出现复发。
