Targa Lucio, Manfredi Jacopo, Tironi Andrea, Gaglione Edoardo, Bianchi Alessandra, Corbara Federico, Muneretto Claudio
U.O. Cardiovascolare, Ospedale Civile, Este (PD), Spedali Civili, Brescia.
Ital Heart J Suppl. 2003 Oct;4(10):862-5.
Papillary fibroelastoma is a rare benign cardiac tumor typically attached to the cardiac valves. The tumor is recognized during life, more often in patients evaluated for embolic events of unclear pathology, but sometimes also in totally asymptomatic patients. There is a general agreement that left-sided fibroelastomas must be removed to avoid systemic complications. Right-sided localization is even rarer. We report a case of a young woman with a papillary fibroelastoma arising from the septal leaflet of the tricuspid valve. It was detected by two-dimensional transthoracic echocardiography and confirmed by transesophageal echocardiography. To our knowledge, this is the seventeenth reported case of a tricuspid valve papillary fibroelastoma, found by means of echocardiography. The tumor was successfully treated by complete surgical excision, without damage of the tricuspid valve. The best therapeutic strategy to be applied in asymptomatic cases is discussed.
乳头状纤维弹性瘤是一种罕见的心脏良性肿瘤,通常附着于心脏瓣膜。该肿瘤在患者生前被发现,更多见于因不明病理的栓塞事件接受评估的患者,但有时也见于完全无症状的患者。人们普遍认为,必须切除左侧纤维弹性瘤以避免全身并发症。右侧定位更为罕见。我们报告一例年轻女性,其乳头状纤维弹性瘤起源于三尖瓣隔叶。通过二维经胸超声心动图检测到该肿瘤,并经食管超声心动图证实。据我们所知,这是通过超声心动图发现的第17例三尖瓣乳头状纤维弹性瘤报告病例。该肿瘤通过完整手术切除成功治疗,三尖瓣未受损伤。本文讨论了应用于无症状病例的最佳治疗策略。