Singh Vijay A, Shariff Masood A, Michael Rami, Azab Basam, Fruchter Shani J, Asgarian Kourosh T, McGinn Joseph T
Eplasty. 2012;12:e28. Epub 2012 Jun 15.
Cardiac papillary fibroelastomas are a rare form of benign, primary cardiac tumor. They tend to develop from the valvular endocardium, with nonvalvular locations being uncommon. They are primarily found on either the mitral or aortic valve. They account for 7% of all primary cardiac tumors. Papillary fibroelastomas are usually identified through either transthoracic echocardiography or transesophageal echocardiography. The latter is more likely to provide a clearer diagnosis. Management remains controversial. The benign histology notwithstanding, the prevailing consensus is toward excision of left-sided cardiac lesions due to the risk of coronary and cerebral embolization. While the diagnosis of cardiac papillary fibroelastomas is relatively rare, the likelihood of encountering a right-sided lesion with rapid growth in a 6-month period is extraordinary. We highlight a case where an 84-year-old man with coronary artery disease was found to have a right atrial mass attached to the tricuspid valve. This mass grew by more than 1 cm in a 6-month period.
心脏乳头状纤维弹性瘤是一种罕见的原发性心脏良性肿瘤。它们往往起源于瓣膜内膜,非瓣膜部位较为少见。主要见于二尖瓣或主动脉瓣。它们占所有原发性心脏肿瘤的7%。乳头状纤维弹性瘤通常通过经胸超声心动图或经食管超声心动图来识别。后者更有可能提供更清晰的诊断。治疗方法仍存在争议。尽管组织学表现为良性,但由于存在冠状动脉和脑栓塞的风险,目前普遍的共识是对左侧心脏病变进行切除。虽然心脏乳头状纤维弹性瘤的诊断相对少见,但在6个月内遇到右侧病变且快速生长的可能性非常罕见。我们重点介绍一例病例,一名患有冠状动脉疾病的84岁男性被发现右心房有一个附着于三尖瓣的肿块。这个肿块在6个月内生长超过了1厘米。