Kelly Aine M, Kazerooni Ella A
Department of Radiology, University of Michigan Medical Center, Ann Arbor, USA.
J Thorac Imaging. 2004 Jan;19(1):52-5. doi: 10.1097/00005382-200401000-00011.
Systemic mastocytosis is an uncommon disease of unknown prevalence. Most patients clinically present with urticaria pigmentosa. The diagnosis is made by finding increased mast cells in the involved tissues. Pulmonary involvement in systemic mastocytosis is rare. The chest radiographic findings include reticulonodular opacities and lung nodules. We present a case of histologically proven pulmonary and skeletal systemic mastocytosis (AKA systemic mast cell disease) associated with a hematologic condition, including the high-resolution computed tomographic findings of this disorder.
系统性肥大细胞增多症是一种患病率不明的罕见疾病。大多数患者临床上表现为色素性荨麻疹。通过在受累组织中发现肥大细胞增多来做出诊断。系统性肥大细胞增多症累及肺部的情况罕见。胸部X线表现包括网状结节状阴影和肺结节。我们报告一例经组织学证实的肺部和骨骼系统性肥大细胞增多症（又称系统性肥大细胞病），该病例与一种血液系统疾病相关，包括该疾病的高分辨率计算机断层扫描结果。
