法洛四联症相关的右冠窦膜性嵴导致的冠状动脉梗阻：晕厥酷似缺氧发作。

Coronary artery obstruction due to membranous ridge of the right sinus valsalva associated with Tetralogy of Fallot: syncope mimics anoxic spell.

作者信息

Shiraishi Isao, Yamagishi Masaaki, Toiyama Kentaro, Osawa Yu, Nakagawa Masao, Takahashi Akiyuki, Shuntoh Keisuke, Hamaoka Kenji

机构信息

Department of Pediatrics, Children's Research Hospital, Kyoto Prefectural University of Medicine, Kyoto, Japan.

出版信息

Ann Thorac Surg. 2004 Jan;77(1):321-2. doi: 10.1016/s0003-4975(03)00751-3.

DOI:10.1016/s0003-4975(03)00751-3

PMID:14726090

Abstract

We report an infant with Tetralogy of Fallot who had suffered from repetitive attacks of syncope without obvious cyanosis. Careful observation by means of echocardiography and angiography revealed that the attacks resulted from acute coronary artery obstruction due to membranous ridge covering the sinus Valsalva. Surgical resection of the abnormal ridge and repair of Tetralogy of Fallot successfully improved the patient's symptoms. Syncope in children should be extensively investigated to exclude obstruction of the coronary arteries.

摘要

我们报告一名患有法洛四联症的婴儿，该婴儿反复出现晕厥发作，无明显紫绀。通过超声心动图和血管造影仔细观察发现，发作是由于覆盖主动脉窦的膜性嵴导致急性冠状动脉阻塞所致。手术切除异常嵴并修复法洛四联症成功改善了患者的症状。对于儿童晕厥应进行广泛检查以排除冠状动脉阻塞。