Pigui Ana, Montembault Sarah, Bonte Eric, Hardin Jean-Michel, Ink Olivier
Service d'Hépato-Gastroentérologie, Centre Hospitalier Général, Soissons.
Gastroenterol Clin Biol. 2003 Nov;27(11):1038-40.
A young woman with type I diabetes mellitus, was hospitalized for a voluminous hepatomegaly associated with hepatocellular glycogen overloading suggesting Mauriac's syndrome. Two factors are involved in the physiopathology of this syndrome, hyperglycemia, and hyperinsulinemia which activates glycogenesis and inhibits glycogenolysis. The prognosis is normally favourable if diabetes is controlled.
一名患有I型糖尿病的年轻女性因肝脏肿大并伴有肝细胞糖原过载（提示Mauriac综合征）而住院。该综合征的病理生理学涉及两个因素，即高血糖和高胰岛素血症，高胰岛素血症会激活糖原生成并抑制糖原分解。如果糖尿病得到控制，预后通常良好。
