• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

伴有高峰失律的婴儿癫痫性脑病(婴儿痉挛症/韦斯特综合征)

Infantile epileptic encephalopathy with hypsarrhythmia (infantile spasms/West syndrome).

作者信息

Hrachovy Richard A, Frost James D

机构信息

Peter Kellaway Section of Neurophysiology, Department of Neurology and Division of Neuroscience, Baylor College of Medicine, One Baylor Plaza, Houston, TX 77030, U.S.A.

出版信息

J Clin Neurophysiol. 2003 Nov-Dec;20(6):408-25. doi: 10.1097/00004691-200311000-00004.

DOI:10.1097/00004691-200311000-00004
PMID:14734931
Abstract

Infantile spasms is a unique disorder peculiar to infancy and early childhood. In this article, the clinical manifestations and electroencephalographic features of the disorder are described. The possible pathophysiologic mechanisms underlying infantile spasms and the relation of this disorder to other childhood encephalopathies are discussed. Finally, the treatment of patients with infantile spasms and their long-term outcome are briefly reviewed.

摘要

婴儿痉挛症是一种婴幼儿特有的独特病症。本文描述了该病症的临床表现和脑电图特征。讨论了婴儿痉挛症潜在的可能病理生理机制以及该病症与其他儿童期脑病的关系。最后,简要回顾了婴儿痉挛症患者的治疗及其长期预后情况。

相似文献

1
Infantile epileptic encephalopathy with hypsarrhythmia (infantile spasms/West syndrome).伴有高峰失律的婴儿癫痫性脑病(婴儿痉挛症/韦斯特综合征)
J Clin Neurophysiol. 2003 Nov-Dec;20(6):408-25. doi: 10.1097/00004691-200311000-00004.
2
[Infantile spasms and modified hypsarrhythmia].[婴儿痉挛症与变异型高峰失律脑电图]
Harefuah. 2011 Apr;150(4):373-7, 418, 417.
3
Infantile spasms syndrome, West syndrome and related phenotypes: what we know in 2013.婴儿痉挛症、韦斯特综合征及相关表型:2013年我们所了解的情况
Brain Dev. 2014 Oct;36(9):739-51. doi: 10.1016/j.braindev.2013.10.008. Epub 2013 Nov 20.
4
West syndrome and other infantile epileptic encephalopathies--Indian hospital experience.韦斯特综合征及其他婴儿癫痫性脑病——印度医院的经验
Brain Dev. 2002 Mar;24(2):130-9. doi: 10.1016/s0387-7604(02)00029-3.
5
Epileptic spasms in clusters without hypsarrhythmia in infancy and childhood: A single age-dependent type of epilepsy or well-defined epileptic syndrome?婴儿和儿童期无高度失律发作的癫痫性痉挛呈簇状:一种单一的年龄依赖性癫痫类型或明确的癫痫综合征?
Epilepsy Res. 2024 May;202:107354. doi: 10.1016/j.eplepsyres.2024.107354. Epub 2024 Mar 20.
6
West syndrome and other infantile epileptic encephalopathies--Indian hospital experience.韦斯特综合征及其他婴儿癫痫性脑病——印度医院的经验
Brain Dev. 2001 Nov;23(7):593-602. doi: 10.1016/s0387-7604(01)00288-1.
7
Infantile spasms.婴儿痉挛症
Pediatr Neurol. 2001 Feb;24(2):89-98. doi: 10.1016/s0887-8994(00)00238-1.
8
The Epilepsy Surgery Experience in Children With Infantile Epileptic Spasms Syndrome at a Tertiary Care Center in Canada.加拿大一家三级保健中心的婴儿痉挛症患儿的癫痫手术经验。
J Child Neurol. 2023 Mar;38(3-4):113-120. doi: 10.1177/08830738231151993. Epub 2023 Feb 14.
9
Epileptic spasms in clusters and associated syndromes other than West syndrome: A study of 48 patients.成簇性癫痫性痉挛及除韦斯特综合征外的相关综合征:48例患者的研究
Epilepsy Res. 2016 Jul;123:29-35. doi: 10.1016/j.eplepsyres.2016.03.006. Epub 2016 Mar 24.
10
Atonic elements combined or uncombined with epileptic spasms in infantile spasms.在婴儿痉挛症中,无张力性发作元素与癫痫性痉挛合并或不合并出现。
Clin Neurophysiol. 2017 Jan;128(1):220-226. doi: 10.1016/j.clinph.2016.11.008. Epub 2016 Nov 20.

引用本文的文献

1
Role of the Ketogenic Diet Therapy and ACTH as Second Treatments in Drug-Resistant Infantile Epileptic Spasms Syndrome.生酮饮食疗法和促肾上腺皮质激素作为二线治疗方法在耐药性婴儿痉挛综合征中的作用
Nutrients. 2025 Jun 23;17(13):2085. doi: 10.3390/nu17132085.
2
Electroclinical characteristics and therapies of tonic spasms.强直性痉挛的电临床特征与治疗方法
Acta Epileptol. 2024 Aug 1;6(1):25. doi: 10.1186/s42494-024-00158-3.
3
Efficacy and tolerability of celastrol and edaravone in the multiple-hit rat model of infantile spasms.雷公藤红素和依达拉奉在婴儿痉挛症多打击大鼠模型中的疗效和耐受性
Epilepsy Behav. 2025 Jan;162:110159. doi: 10.1016/j.yebeh.2024.110159. Epub 2024 Nov 21.
4
Electroclinical Features of Infantile Epileptic Spasms Syndrome.婴儿痉挛症综合征的电临床特征
Ann Indian Acad Neurol. 2024 May 1;27(3):227-235. doi: 10.4103/aian.aian_445_24. Epub 2024 Jun 24.
5
Interictal EEG features as computational biomarkers of West syndrome.发作间期脑电图特征作为韦斯特综合征的计算生物标志物。
Front Pediatr. 2024 Jun 5;12:1406772. doi: 10.3389/fped.2024.1406772. eCollection 2024.
6
Hypsarrhythmia and triphasic waves seem to be akin(similar) age-dependent responses of the brain to different insults.高峰节律紊乱和三相波似乎是大脑对不同损伤的类似(相似)的年龄依赖性反应。
J Neurosci Rural Pract. 2024 Jan-Mar;15(1):156-158. doi: 10.25259/JNRP_319_2023. Epub 2023 Oct 24.
7
West Syndrome and the Importance of Routine Physical Examinations and Parental Education: A Case Report.韦斯特综合征与常规体格检查及家长教育的重要性:一例报告
Cureus. 2022 Nov 24;14(11):e31848. doi: 10.7759/cureus.31848. eCollection 2022 Nov.
8
Neurobehavioral deficits and a progressive ictogenesis in the tetrodotoxin model of epileptic spasms.神经行为缺陷和托烷司琼模型中癫痫痉挛的进行性发作。
Epilepsia. 2022 Dec;63(12):3078-3089. doi: 10.1111/epi.17428. Epub 2022 Oct 12.
9
Asymmetric epileptic spasms after corpus callosotomy in children with West syndrome may be a good indicator for unilateral epileptic focus and subsequent resective surgery.儿童脑性瘫痪手术后出现非对称性癫痫痉挛可能是单侧癫痫灶和随后的切除术的一个良好指标。
Epilepsia Open. 2022 Sep;7(3):474-487. doi: 10.1002/epi4.12631. Epub 2022 Aug 1.
10
Discrimination of secondary hypsarrhythmias to Zika virus congenital syndrome and west syndrome based on joint moments and entropy measurements.基于关节力矩和熵测量对寨卡病毒先天性综合征和west 综合征的继发高度失律进行鉴别。
Sci Rep. 2022 May 5;12(1):7389. doi: 10.1038/s41598-022-11395-2.