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转移性先天性骶尾部皮下室管膜瘤。

Metastasising congenital subcutaneous sacrococcygeal ependymoma.

作者信息

Gupta R K, Pratap D

机构信息

Postgraduate Department of Pathology, M.L.B. Medical College, Jhansi, India.

出版信息

Indian J Cancer. 1992 Jun;29(2):76-81.

PMID:1473837
Abstract

A case of myxopapillary ependymoma located subcutaneously in sacrococcygeal area of a 18 months male child with metastasis to right inguinal lymph nodes is described; the tumour was present since birth. Histological examination of the tumour besides myxopapillary structures, also revealed an ependyma lined cystic space, resembling ventricular cavity. So far only two cases of congenital metastasising subcutaneous sacrococcygeal ependymoma have been described. However, the present case had a very aggressive post-operative biological behaviour.

摘要

描述了一例18个月大男童骶尾部皮下黏液乳头型室管膜瘤伴右腹股沟淋巴结转移的病例;该肿瘤自出生就存在。肿瘤的组织学检查除黏液乳头结构外,还发现一个由室管膜衬里的囊性腔隙,类似脑室腔。迄今为止,仅报道过两例先天性转移性骶尾部皮下室管膜瘤。然而,本例具有非常侵袭性的术后生物学行为。

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Spinal Metastasis from Subcutaneous Sacrococcygeal Ependymoma: A Case Report with Long-Term Follow-Up.骶尾部皮下室管膜瘤脊柱转移:1例长期随访病例报告
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