以肾上腺功能不全为表现的原发性肾上腺淋巴瘤。病例报告及文献复习。

Primary adrenal lymphoma presenting as adrenal insufficiency. A case report and review of literature.

作者信息

Zar Tausif, Khan Faraz, Petit William, Bernene James R

机构信息

Department of Medicine, University of Connecticut, USA.

出版信息

Conn Med. 2004 Jan;68(1):7-10.

PMID:14752912

Abstract

Primary adrenal lymphoma (PAL) with adrenal insufficiency is a rare entity that has a unique presentation and prognosis when compared to other high-grade B-cell Non-Hodgkin's Lymphomas (NHL). Radiologic characteristics and image-guided biopsy are helpful in diagnosis. Current chemotherapy of choice is CHOP [Cyclophosphamide, Hydroxydaunomycin (doxorubicin), Oncovin (vincristine sulfate) and Prednisone]. More cases need to be documented to formulate an effective approach to PAL.

摘要

伴有肾上腺功能不全的原发性肾上腺淋巴瘤（PAL）是一种罕见的疾病，与其他高级别B细胞非霍奇金淋巴瘤（NHL）相比，具有独特的表现和预后。放射学特征及影像引导下活检有助于诊断。目前的化疗首选方案是CHOP[环磷酰胺、羟基柔红霉素（阿霉素）、长春新碱（硫酸长春新碱）和泼尼松]。需要记录更多病例，以制定针对原发性肾上腺淋巴瘤的有效治疗方法。