Chauke Risenga Frank, Muthuphei M Nelson
Department of Cardiothoracic Surgery, Medical University of Southern Africa, Ga-Rankuwa Hospital, Pretoria.
S Afr J Surg. 2003 Nov;41(4):92-4.
A 4-year-old girl presented with an intrathoracic tumour that was pleural in origin, invading the right lower lobe. The patient underwent urgent right thoracotomy and surgical excision of the tumour and right lower lobectomy as the tumour was invading that lobe. The histological report initially reported it as a rhabdomyosarcoma, embryonal type, but after consultation it was changed to type III pleuropulmonary blastoma. The patient was treated with chemotherapy but succumbed to the disease 12 months after the diagnosis. Relevant literature on pleuropulmonary blastoma is reviewed.
一名4岁女孩出现起源于胸膜的胸腔内肿瘤，侵犯右下叶。由于肿瘤侵犯该叶，患者接受了紧急右开胸手术及肿瘤切除和右下叶切除术。组织学报告最初将其诊断为胚胎型横纹肌肉瘤，但经会诊后改为III型胸膜肺母细胞瘤。患者接受了化疗，但在诊断后12个月死于该疾病。本文对胸膜肺母细胞瘤的相关文献进行了综述。
