Fujikawa K, Onishi H, Yoshimura N, Arai Y, Hashimura T, Yoshida O
Department of Urology, Faculty of Medicine, Kyoto University.
Hinyokika Kiyo. 1992 Oct;38(10):1179-82.
Sacral agenesis is an uncommon disease. About 50 cases have been reported in Japan since 1929. Neurogenic bladder is often accompanied with the disease. The patient was a 26-year-old man who had suffered from persistent urinary incontinence since his childhood. Kidney-ureter-bladder (KUB) revealed Type IV sacral agenesis according to the classification by Renshaw. The upper urinary tract remained normal. Urodynamics study showed a low compliance bladder with low urethral pressure. Pharmacotherapy failed to improve his continence. Augmentation sigmoid-cystoplasty was undertaken to enlarge vesical capacity and it has successfully overcome his urinary incontinence. Clinical aspects of sacral agenesis are discussed focusing on urological problems.
骶骨发育不全是一种罕见疾病。自1929年以来，日本已报告约50例。神经源性膀胱常伴有该疾病。患者为一名26岁男性，自幼患有持续性尿失禁。根据伦肖的分类，肾脏-输尿管-膀胱（KUB）显示为IV型骶骨发育不全。上尿路保持正常。尿动力学研究显示膀胱顺应性低且尿道压力低。药物治疗未能改善其尿失禁情况。遂进行乙状结肠膀胱扩大术以增加膀胱容量，成功克服了他的尿失禁问题。本文围绕泌尿系统问题，对骶骨发育不全的临床情况进行了讨论。
