Gobernado J M, Galarreta M, De Blas G, Jimenez-Escrig A, Hernandez A
Neurology Service, Ramon y Cajal Hospital, Madrid, Spain.
Mov Disord. 1992 Oct;7(4):367-9. doi: 10.1002/mds.870070413.
Isolated continuous lingual myoclonus is an exceptional entity, poorly documented and understood. A patient with a nonepileptic continuous rhythmical myoclonus, affecting the anterior portion of the tongue, as an independent involuntary disorder, is reported. Electromyography showed low frequency (2-4 Hz) bursts of genioglossus muscles activity. The EEG, visual, auditory and somatosensory evoked responses were normal. Imaging techniques like CT and MRI failed to reveal any brainstem or cerebellar lesion. Lingual myoclonus showed a very good response to sodium valproate.
孤立性持续性舌肌阵挛是一种罕见的病症，相关文献记载和了解较少。本文报告了一例患者，其患有非癫痫性持续性节律性肌阵挛，累及舌前部，为一种独立的自主神经功能障碍。肌电图显示颏舌肌肌肉活动呈低频（2 - 4赫兹）爆发。脑电图、视觉、听觉和体感诱发电位均正常。CT和MRI等影像学检查未发现任何脑干或小脑病变。舌肌阵挛对丙戊酸钠反应良好。
