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Plasma thromboplastin component (PTC) deficiency; a new disease resembling hemophilia.

作者信息

AGGELER P M, WHITE S G, GLENDENING M B, PAGE E W, LEAKE T B, BATES G

出版信息

Proc Soc Exp Biol Med. 1952 Apr;79(4):692-4. doi: 10.3181/00379727-79-19488.

DOI:10.3181/00379727-79-19488
PMID:14920537
Abstract
摘要

相似文献

1
Plasma thromboplastin component (PTC) deficiency; a new disease resembling hemophilia.血浆凝血活酶成分(PTC)缺乏症;一种类似血友病的新疾病。
Proc Soc Exp Biol Med. 1952 Apr;79(4):692-4. doi: 10.3181/00379727-79-19488.
2
Use of purified prothrombin in the study of hemophilia and plasma thromboplastin component (PTC) deficiency.纯化凝血酶原在血友病及血浆凝血活酶成分(PTC)缺乏症研究中的应用。
J Appl Physiol. 1954 Jan;6(7):429-36. doi: 10.1152/jappl.1954.6.7.429.
3
Plasma thromboplastin component (PTC), a hitherto unrecognized blood coagulation factor; case report of PTC deficiency.血浆凝血活酶成分(PTC),一种迄今未被认识的凝血因子;PTC缺乏症的病例报告。
Blood. 1953 Feb;8(2):101-24.
4
Deuterohemophilia: plasma thromboplastin factor B deficiency: plasma thromboplastin component (PTC) deficiency, Christmas disease, hemophilia B.
Blood. 1954 Mar;9(3):246-53.
5
Plasma thromboplastin component (PTC) deficiency produced by prolonged administration or prothrombopenic anticoagulants.长期使用促凝血酶原减少性抗凝剂导致血浆凝血活酶成分(PTC)缺乏。
Proc Soc Exp Biol Med. 1955 May;89(1):81-3. doi: 10.3181/00379727-89-21721.
6
[Hemophilia B; two cases of hereditary hemophilia due to a deficiency of a new clotting factor (Christmas factor)].
Acta Haematol. 1953 Aug;10(2):64-76.
7
[Congenital deficiency of factor IX (Christmas, PTC); hemophilia B].[先天性因子IX缺乏症(克里斯马斯病、血浆凝血活酶成分缺乏症);血友病B]
Vnitr Lek. 1955 Mar;1(3):179-82.
8
PLASMA THROMBOPLASTIN COMPONENT (PTC) DEFICIENCY: A CASE REPORT.血浆凝血活酶成分(PTC)缺乏症:一例报告。
Shonika Kiyo. 1963 Sep-Oct;9:297-301.
9
[Hemophilic syndrome of associated antihemophilic globulin and plasma thromboplastin component deficiencies].
Haematologica. 1955;40:391-422.
10
Hemorrhagic diathesis due to PTC (plasma thromboplastin component) deficiency.因血浆凝血活酶成分(PTC)缺乏所致的出血素质
Proc Soc Exp Biol Med. 1953 Mar;82(3):445-8. doi: 10.3181/00379727-82-20142.

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J Clin Med. 2022 Aug 22;11(16):4932. doi: 10.3390/jcm11164932.
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J Blood Med. 2020 Dec 17;11:457-463. doi: 10.2147/JBM.S289390. eCollection 2020.
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Enhanced Factor IX Activity following Administration of AAV5-R338L "Padua" Factor IX versus AAV5 WT Human Factor IX in NHPs.在非人灵长类动物中给予AAV5-R338L“帕多瓦”因子IX与AAV5野生型人因子IX后,因子IX活性增强。
Mol Ther Methods Clin Dev. 2019 Sep 26;15:221-231. doi: 10.1016/j.omtm.2019.09.005. eCollection 2019 Dec 13.
5
Extravascular FIX and coagulation.血管外凝血因子IX与凝血
Thromb J. 2016 Oct 4;14(Suppl 1):35. doi: 10.1186/s12959-016-0104-2. eCollection 2016.
6
Characterization of IXINITY® (Trenonacog Alfa), a Recombinant Factor IX with Primary Sequence Corresponding to the Threonine-148 Polymorph.IXINITY®(重组凝血因子IXa)的特性,其一级序列对应苏氨酸-148多态性。
Adv Hematol. 2016;2016:7678901. doi: 10.1155/2016/7678901. Epub 2016 Feb 21.
7
Adeno-associated viral vectors for the treatment of hemophilia.用于治疗血友病的腺相关病毒载体。
Hum Mol Genet. 2016 Apr 15;25(R1):R36-41. doi: 10.1093/hmg/ddv475. Epub 2015 Nov 27.
8
Animal models of hemophilia.血友病动物模型。
Prog Mol Biol Transl Sci. 2012;105:151-209. doi: 10.1016/B978-0-12-394596-9.00006-8.
9
Concerning the Functions and Nomenclature of Blood Clotting Factors.关于凝血因子的功能及命名
Trans Am Clin Climatol Assoc. 1959;70:67-74.
10
Inheritance of Haemophilia.血友病的遗传
Br Med J. 1956 Mar 24;1(4968):675-6.