Ismail J B
Haemolytic Anaemia Unit, Ripas Hospital, Bandar Seri Begawan, Brunei Darussalam.
Med J Malaysia. 1992 Jun;47(2):98-102.
One thousand consecutive Brunei Darussalam patients referred with low Hb, and/or low MCV and MCH (Hb < 12.5g/dl, MCV < 76fl, MCH < 27pg) were studied in the laboratory for underlying haemoglobinopathies. 30.0% of such patients were proved to have either beta-thalassaemia trait, beta-thalassaemia major, Hb AE, Hb EE, Hb E beta-thalassaemia or Hb H disease. In some, the haemoglobin abnormality was not identified precisely. Alpha-thalassaemia was suspected in an additional 4.3% of cases but confirmation study by globin-chain synthesis was not available. Beta-thalassaemia trait which was the predominant disorder was equally distributed among the three major race groups of Brunei Darussalam. Hb E was found exclusive among the Malay population. Hb H disease appeared as more common among the Chinese or the Malays (p > 0.05). This study reveals that thalassaemia and haemoglobinopathies are prevalent in Brunei Darussalam.
对一千名因血红蛋白(Hb)低和/或平均红细胞体积(MCV)及平均红细胞血红蛋白含量(MCH)低(Hb < 12.5g/dl,MCV < 76fl,MCH < 27pg)而前来就诊的文莱达鲁萨兰国患者进行了实验室检查,以确定其潜在的血红蛋白病。结果显示,30.0%的此类患者被证实患有β地中海贫血特征、重型β地中海贫血、Hb AE、Hb EE、Hb Eβ地中海贫血或Hb H病。在一些患者中,血红蛋白异常未得到精确鉴定。另外4.3%的病例怀疑患有α地中海贫血,但无法通过珠蛋白链合成进行确诊研究。作为主要疾病的β地中海贫血特征在文莱达鲁萨兰国的三大主要种族群体中分布均匀。Hb E仅在马来人群中发现。Hb H病在华人或马来人中更为常见(p > 0.05)。这项研究表明,地中海贫血和血红蛋白病在文莱达鲁萨兰国很普遍。