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[230例颅底凹陷症和Arnold-Chiari畸形患者的自主神经系统障碍]

[Autonomic nervous system disorders in 230 cases of basilar impression and Arnold-Chiari deformity].

作者信息

da Silva J A, Brito J C, da Nóbrega P V

机构信息

Neurochirurgische Klinik, Universität Paraíba in João Pessoa, Brasilien.

出版信息

Neurochirurgia (Stuttg). 1992 Nov;35(6):183-8.

PMID:1494411
Abstract

Within the period of 1971 to 1989 we operated on 230 cases of craniocervical malformations characterised by 189 cases of basilar impression associated with Arnold-chiari malformation, 28 cases of isolated basilar impression and 13 cases of Arnold-Chiari malformation. Autonomic disturbance was observed in 136 (59.1%) cases: sexual disorders like reduced potency and impotency were observed in 86 (60.9%) out of 141 male patients, urinary symptoms in 39 (17%) patients; and other autonomic features like dyspnea, anhidrosis, hyperhidrosis, Claude Bernard-Horner syndrome and constipation in 41 (17.8%) patients.

摘要

在1971年至1989年期间,我们对230例颅颈畸形患者进行了手术,其中包括189例合并Arnold - Chiari畸形的基底凹陷症、28例孤立性基底凹陷症和13例Arnold - Chiari畸形。136例(59.1%)患者出现自主神经功能障碍:141例男性患者中有86例(60.9%)出现性功能障碍,如性欲减退和阳痿;39例(17%)患者出现泌尿系统症状;41例(17.8%)患者出现其他自主神经功能特征,如呼吸困难、无汗、多汗、Claude Bernard - Horner综合征和便秘。

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