Della Valle Daniella, Chevitarese Ana Beatriz Alonso, Maia Lucianne Cople, Farinhas Joao Alfredo
Cidade Universitária Ilha do Governador, Rio de Janeiro, RJ, Brazil.
J Clin Pediatr Dent. 2004 Winter;28(2):103-6. doi: 10.17796/jcpd.28.2.55021560w701h2r2.
The ectodermal dysplasia constitutes a group of hereditary disorders whose clinical manifestations can be defects in ectodermal structures. The hypohidrotic and anihidrotic are commonly types of ectodermal dysplasia. The main characteristics are dental anomalies, hypotrichosis and hypohidrosis. The oral rehabilitation of this patients is important for better social living, self esteem and oral function. This paper had as objective to relate and discuss a case of anihidrotic ectodermal dysplasia, describing the positive influence of an alternative rehabilitation treatment.
外胚层发育异常构成一组遗传性疾病，其临床表现可能为外胚层结构缺陷。少汗型和无汗型通常是外胚层发育异常的类型。主要特征是牙齿异常、毛发稀少和少汗。对这类患者进行口腔修复对于改善社会生活、自尊和口腔功能非常重要。本文旨在关联并讨论一例无汗型外胚层发育异常病例，描述一种替代性修复治疗的积极影响。
