Gamblin T Clark, Stephens Richard E, Johnson Richard K, Rothwell Michael
Department of Surgery, Mercer University School of Medicine, Medical Center of Central Georgia, Macon, Georgia 31201, USA.
Curr Surg. 2003 Sep-Oct;60(5):517-20. doi: 10.1016/S0149-7944(03)00030-8.
Midgut malrotation is an anomaly of fetal intestinal rotation that usually presents in the first month of life. It is rare for malrotation to present in adulthood. Symptomatic patients present either acutely with bowel obstruction and intestinal ischemia with a midgut or cecal volvulus, or chronically with vague abdominal pain. Chronic symptoms can often make the diagnosis difficult. Findings diagnostic of malrotation are described using several modalities such as barium studies, computed tomography (CT) scans, angiography, and often emergent laparotomy. Treatment remains the Ladd procedure originally described by Dr. Ladd in 1936. Complete resolution of acute obstruction or chronic abdominal pain is the result of a high index of suspicion for malrotation, appropriate diagnostic studies, and aggressive definitive surgical treatment. We present a case of malrotation in an adult who presented with chronic abdominal pain. Midgut malrotation is a congenital anomaly referring to either lack of or incomplete rotation of the fetal intestines around the axis of the superior mesenteric artery during fetal development. Most patients present with bilious vomiting in the first month of life because of duodenal obstruction or a volvulus. It is rare for this condition to present in adulthood. The true incidence in adults is difficult to estimate because most patients who remain are asymptomatic and their conditions are, therefore, never diagnosed. A literature review by von Flue et al cites 40 cases from 1923 to 1992. Patients who are symptomatic often present either acutely with bowel obstruction and intestinal ischemia with a midgut or cecal volvulus or chronically with vague abdominal pain. These symptoms are caused by peritoneal bands first described by Ladd in 1932. These bands run from the cecum to the right lateral abdominal wall. We present a case of malrotation in an adult who presented with chronic abdominal pain.
中肠旋转不良是一种胎儿肠道旋转异常,通常在出生后的第一个月出现。在成年期出现旋转不良的情况很少见。有症状的患者要么急性出现肠梗阻和肠缺血伴中肠或盲肠扭转,要么慢性出现模糊的腹痛。慢性症状常常使诊断困难。使用多种检查手段来描述旋转不良的诊断结果,如钡剂造影、计算机断层扫描(CT)、血管造影,通常还需要急诊剖腹手术。治疗仍然是1936年Ladd医生最初描述的Ladd手术。对旋转不良保持高度怀疑、进行适当的诊断检查以及积极的确定性手术治疗,才能使急性梗阻或慢性腹痛完全缓解。我们报告一例成年患者出现慢性腹痛,诊断为中肠旋转不良。中肠旋转不良是一种先天性异常,指胎儿发育过程中肠道围绕肠系膜上动脉轴缺乏或不完全旋转。大多数患者在出生后的第一个月因十二指肠梗阻或扭转而出现胆汁性呕吐。这种情况在成年期出现很罕见。成人的真实发病率难以估计,因为大多数患者没有症状,因此他们的病情从未被诊断出来。von Flue等人的文献综述引用了1923年至1992年的40个病例。有症状的患者通常要么急性出现肠梗阻和肠缺血伴中肠或盲肠扭转,要么慢性出现模糊的腹痛。这些症状是由1932年Ladd首次描述的腹膜带引起的。这些带子从盲肠延伸至右侧腹壁。我们报告一例成年患者出现慢性腹痛,诊断为中肠旋转不良。