苏萨克综合征：4例报告及文献综述
Susac syndrome: report of four cases and review of the literature.
作者信息
Do Tai Hung, Fisch Christiane, Evoy François
机构信息
Department of Radiology, CHUS-Hôpital Fleurimont, Sherbrooke, Quebec, Canada.
出版信息
AJNR Am J Neuroradiol. 2004 Mar;25(3):382-8.
Abstract
Susac syndrome is a rare disease of unknown pathogenesis. It is caused by a microangiopathy affecting the arterioles of the brain, retina, and cochlea, giving the classic clinical triad of subacute encephalopathy, visual loss secondary to retinal branch occlusions, and sensorineural hearing loss. The features of four cases of this syndrome are presented. MR imaging, retinal fluorescein angiography, and audiography findings enable diagnosis. Early therapy may reduce sequelae and improve recovery.
摘要
Susac综合征是一种发病机制不明的罕见疾病。它由一种影响脑、视网膜和耳蜗小动脉的微血管病引起，具有典型的临床三联征，即亚急性脑病、视网膜分支阻塞继发的视力丧失和感音神经性听力损失。本文介绍了4例该综合征的病例特点。磁共振成像、视网膜荧光血管造影和听力检查结果有助于诊断。早期治疗可能会减少后遗症并促进康复。
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本文引用的文献
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Recurrence of Susac syndrome (retinocochleocerebral vasculopathy) after remission of 18 years.Susac综合征（视网膜-耳蜗-脑微血管病）缓解18年后复发。
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Susac syndrome.苏萨克综合征
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A microangiopathic syndrome of encephalopathy, hearing loss, and retinal arteriolar occlusions.一种伴有脑病、听力丧失和视网膜小动脉闭塞的微血管病综合征。
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