苏萨克综合征：最新综述
Susac's Syndrome: An Updated Review.
作者信息
Pereira Sara, Vieira Bruna, Maio Tiago, Moreira Jorge, Sampaio Filipa
机构信息
Department of Ophthalmology, Hospital Pedro Hispano, Matosinhos, Portugal.
出版信息
Neuroophthalmology. 2020 May 1;44(6):355-360. doi: 10.1080/01658107.2020.1748062. eCollection 2020.
Abstract
Susac's syndrome is a rare immune-mediated endotheliopathy that mainly affects young women. It is characterised by the presence of encephalopathy, retinal vaso-occlusive disease and hearing loss. Diagnosis is based on the clinical presentation, brain magnetic resonance imaging, retinal fluorescein angiography, and audiometry. Treatment consists of immunosuppressive therapy. This review focuses on recent developments in the diagnosis and management of the condition.
摘要
苏萨克综合征是一种罕见的免疫介导性内皮病变，主要影响年轻女性。其特征为存在脑病、视网膜血管闭塞性疾病和听力损失。诊断基于临床表现、脑磁共振成像、视网膜荧光血管造影和听力测定。治疗包括免疫抑制治疗。本综述重点关注该疾病诊断和管理方面的最新进展。
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