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Recurrent Branch Retinal Artery Occlusions Revealing Susac's Syndrome.复发性视网膜动脉分支阻塞揭示Susac综合征
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本文引用的文献

1
The Utility of Fundus Fluorescein Angiography in Neuro-Ophthalmology.眼底荧光血管造影在神经眼科中的应用
Neuroophthalmology. 2019 Aug 21;43(4):217-234. doi: 10.1080/01658107.2019.1604764. eCollection 2019 Aug.
2
A review and update on the ophthalmic implications of Susac syndrome.Susac 综合征眼科学相关问题的综述及更新。
Surv Ophthalmol. 2019 Jul-Aug;64(4):477-485. doi: 10.1016/j.survophthal.2019.01.007. Epub 2019 Jan 29.
3
Otologic manifestations of Susac syndrome.Susac 综合征的耳科学表现。
Acta Otorhinolaryngol Ital. 2018 Dec;38(6):544-553. doi: 10.14639/0392-100X-2166.
4
Diagnostic Criteria and Treatment Algorithm for Susac Syndrome.Susac 综合征的诊断标准和治疗算法。
J Neuroophthalmol. 2019 Mar;39(1):60-67. doi: 10.1097/WNO.0000000000000677.
5
Characteristics of headache in relation to the manifestation of Susac syndrome.与Susac综合征表现相关的头痛特征
Medicina (Kaunas). 2017;53(6):420-425. doi: 10.1016/j.medici.2018.01.003. Epub 2018 Feb 3.
6
Retinal Arterio-Arterial Collaterals in Susac Syndrome.Susac 综合征中的视网膜小动脉-小动脉吻合支。
J Neuroophthalmol. 2018 Dec;38(4):459-461. doi: 10.1097/WNO.0000000000000627.
7
Guidelines for treatment of Susac syndrome - An update.Susac 综合征治疗指南——更新版。
Int J Stroke. 2020 Jul;15(5):484-494. doi: 10.1177/1747493017751737. Epub 2018 Jan 10.
8
Anatomical and functional correlation in Susac syndrome: multimodal imaging assessment.Susac综合征的解剖与功能相关性:多模态成像评估
Int J Retina Vitreous. 2017 Oct 16;3:39. doi: 10.1186/s40942-017-0092-9. eCollection 2017.
9
Susac Syndrome: A differential diagnosis of white matter lesions.Susac综合征:白质病变的鉴别诊断。
Mult Scler Relat Disord. 2017 Jul;15:42-46. doi: 10.1016/j.msard.2017.04.007. Epub 2017 May 3.
10
Susac syndrome: clinical characteristics, clinical classification, and long-term prognosis.苏萨克综合征:临床特征、临床分类及长期预后。
Medicine (Baltimore). 2016 Oct;95(43):e5223. doi: 10.1097/MD.0000000000005223.

苏萨克综合征:最新综述

Susac's Syndrome: An Updated Review.

作者信息

Pereira Sara, Vieira Bruna, Maio Tiago, Moreira Jorge, Sampaio Filipa

机构信息

Department of Ophthalmology, Hospital Pedro Hispano, Matosinhos, Portugal.

出版信息

Neuroophthalmology. 2020 May 1;44(6):355-360. doi: 10.1080/01658107.2020.1748062. eCollection 2020.

DOI:10.1080/01658107.2020.1748062
PMID:33408428
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7746245/
Abstract

Susac's syndrome is a rare immune-mediated endotheliopathy that mainly affects young women. It is characterised by the presence of encephalopathy, retinal vaso-occlusive disease and hearing loss. Diagnosis is based on the clinical presentation, brain magnetic resonance imaging, retinal fluorescein angiography, and audiometry. Treatment consists of immunosuppressive therapy. This review focuses on recent developments in the diagnosis and management of the condition.

摘要

苏萨克综合征是一种罕见的免疫介导性内皮病变,主要影响年轻女性。其特征为存在脑病、视网膜血管闭塞性疾病和听力损失。诊断基于临床表现、脑磁共振成像、视网膜荧光血管造影和听力测定。治疗包括免疫抑制治疗。本综述重点关注该疾病诊断和管理方面的最新进展。