Savaş Hatice, Karabacakoğlu Aydin, Karaköse Serdar, Durmuş Ercan
Selçuk Universitesi Meram Tip Fakültesi, Radyoloji Anabilim Dali, Konya, Turkey.
Tani Girisim Radyol. 2004 Mar;10(1):39-43.
Neurofibromatosis type 1 is the most common autosomal dominant disorder of the nerve sheath and best defined phakomatosis. It usually affects skeletal system, central nervous system, eye, endocrine gland and cardiovascular system. Gingival involvement is very rare. We report radiological findings of three patients with plexiform neurofibroma who had diffuse, unilateral gingival involvement.
1型神经纤维瘤病是最常见的常染色体显性神经鞘疾病,也是定义最明确的错构瘤病。它通常影响骨骼系统、中枢神经系统、眼睛、内分泌腺和心血管系统。牙龈受累非常罕见。我们报告了3例患有丛状神经纤维瘤且有弥漫性单侧牙龈受累患者的影像学表现。