Manconi R, Bolla G, Pavon I
Servizio di Anatomia Patologica, ASL 13, Ospedale di Dolo (VE).
Pediatr Med Chir. 2003 Sep-Oct;25(5):364-6.
The Authors describe a very rare congenital case of bronchogenic subcutaneous cyst of the scapular region occurring in a 8-year-old girl. Only 8 other cases have been published so far. The cyst was asymptomatic and was surgically removed. It measured 2.3 cm. in diameter. Histologically, the cyst was lined by ciliated columnar pseudostratified epithelium devoid of goblet cells and mucus secreting cells. The epithelium lacked immunoreactivity for estrogen and progesterone receptors. The cyst wall contained smooth muscle bundles, but cartilage was absent. Differential diagnosis with emphasis on cutaneous ciliated cyst (Mullerian cyst) is discussed. It appears conceivable that cutaneous ciliated bronchogenic cysts may show partial or fully developed features indicating their bronchial origin.
作者描述了一例非常罕见的先天性肩胛区支气管源性皮下囊肿病例，患者为一名8岁女孩。迄今为止，仅发表过8例其他病例。该囊肿无症状，已通过手术切除。其直径为2.3厘米。组织学检查显示，囊肿内衬为无杯状细胞和黏液分泌细胞的纤毛柱状假复层上皮。该上皮对雌激素和孕激素受体缺乏免疫反应性。囊肿壁含有平滑肌束，但无软骨。文中讨论了与皮肤纤毛囊肿（苗勒管囊肿）的鉴别诊断。皮肤纤毛支气管源性囊肿可能呈现出部分或完全发育的特征，表明其支气管起源，这似乎是可以想象的。
