Köylüoğlu Gökhan, Yildiz Esin, Koyuncu Ayhan, Atalar Mehmet
Department of Pediatric Surgery, Cumhuriyet University, Faculty of Medicine, Sivas, Turkey.
J Pediatr Surg. 2004 Apr;39(4):640-2. doi: 10.1016/j.jpedsurg.2003.12.025.
Intraabdominal fibromatosis is an uncommon neoplasm. The aggressive nature of these tumors and the potential for major morbidity secondary to resection can present a difficult surgical dilemma. A 9-year-old boy presented with anemia and vomiting. He had esophagogastric fibromatosis diagnosed and underwent distal esophagectomy, total gastrectomy, Hunt-Lawrence jejunal pouch, and Roux-en-Y esophagojejunostomy. This report describes the successful surgical management of an esophagogastric fibromatosis for the first time in the English-language literature. The management of this tumor is discussed with particular regard to the very unusual clinical presentation.
腹腔内纤维瘤病是一种罕见的肿瘤。这些肿瘤的侵袭性以及切除术后继发严重并发症的可能性会带来棘手的手术难题。一名9岁男孩出现贫血和呕吐症状。他被诊断为食管胃纤维瘤病,并接受了远端食管切除术、全胃切除术、亨特-劳伦斯空肠袋术以及 Roux-en-Y 食管空肠吻合术。本报告首次在英文文献中描述了食管胃纤维瘤病成功的手术治疗。本文特别针对这种非常不寻常的临床表现对该肿瘤的治疗进行了讨论。