van Hagen C C, Carbasius Weber E, van den Hurk Th A M, Oudshoorn J H, Dorland L, Berger R, de Koning T
Department of Metabolic Diseases, University Medical Centre Utrecht, The Netherlands.
J Inherit Metab Dis. 2004;27(1):111-2. doi: 10.1023/b:boli.0000016678.78134.7d.
Resting energy expenditure (REE) was investigated in 8 children with propionic and methylmalonic acidaemias because a lowered REE has been reported in the literature. We observed a marginally elevated REE and think that adequate caloric intake and the use of a synthetic amino acid mixture are responsible for this.
