Khiari K, Cherif L, Hadj Ali I, Turki S, Lakhoua Y, Ben Abdallah N, Ben Maïz H
Service de Néphrologie et de Médecine interne, Unité d'Endocrinologie, Hôpital Charles Nicolle, boulevard du 9 Avril, 1006 Tunis, Tunisia.
Ann Endocrinol (Paris). 2003 Dec;64(6):426-7.
Vasculitis with central diabetes insipidus is a rare condition which must be recognized for an appropriate management. We report a case of Behçet disease with central diabetes insipidus. A forty seven year old men presented recurring oral and genital ulcers, skin lesions, polyarthralgia. Two years later, he showed right uveitis and central diabetes insipidus without dysfunction of the pituitary gland. Computed tomographic scan showed normal neurohypophysis and pituitary gland. Later on, he presented hemiplegia. The cerebral computed tomographic scan showed hypodense lesions. Central diabetes insipidus should not be systematically searched because it is a rare feature of the Behçet disease.
伴有中枢性尿崩症的血管炎是一种罕见疾病,必须予以识别以便进行恰当治疗。我们报告一例伴有中枢性尿崩症的白塞病病例。一名47岁男性出现复发性口腔和生殖器溃疡、皮肤损害、多关节痛。两年后,他出现右眼葡萄膜炎和中枢性尿崩症,垂体无功能障碍。计算机断层扫描显示神经垂体和垂体正常。后来,他出现偏瘫。脑部计算机断层扫描显示低密度病变。中枢性尿崩症不应被常规排查,因为它是白塞病的一种罕见特征。