Tobe Satoshi, Nohara Hideaki, Yoshida Kazunori, Tanimura Nobuhiro, Kurokawa Ryohei, Kawata Masahito
Department of Cardiovascular Surgery, Akashi Medical Center, 743-33 Yagi, Okubo-cho, Akashi, Hyogo 674-0063, Japan.
Jpn J Thorac Cardiovasc Surg. 2004 Mar;52(3):139-42. doi: 10.1007/s11748-004-0130-z.
Primary pulmonary artery sarcoma is extremely rare and a lethal tumor. Complete resection of the tumor and following adequate reconstruction is the only hope for cure and prolonged survival. We report a case of successful surgical excision of primary pulmonary artery sarcoma involving pulmonary trunk, pulmonary valve and right ventricular outflow tract wall, which were replaced with prosthetic valved conduit. Postoperative histopathological diagnosis was leiomyosarcoma. The patient is well without any evidence of recurrence at 10 months after surgery.
原发性肺动脉肉瘤极为罕见,是一种致命性肿瘤。完整切除肿瘤并进行充分的重建是治愈和延长生存期的唯一希望。我们报告一例成功手术切除累及肺动脉干、肺动脉瓣和右心室流出道壁的原发性肺动脉肉瘤的病例,这些部位用带瓣人工血管进行了置换。术后组织病理学诊断为平滑肌肉瘤。患者术后10个月情况良好,无任何复发迹象。