马尾原发性原始神经外胚层肿瘤伴颅内播散。

Primary primitive neuro-ectodermal tumor of cauda equina with intracranial seeding.

作者信息

Akyüz M, Demiral A N, Gürer I E, Uçar T, Tuncer R

机构信息

Department of Neurosurgery, Akdeniz University Medical School, Antalya, Turkey.

出版信息

Acta Neurochir (Wien). 2004 May;146(5):525-8. doi: 10.1007/s00701-003-0212-1. Epub 2004 Mar 22.

DOI:10.1007/s00701-003-0212-1

PMID:15118892

Abstract

Primitive neuro-ectodermal tumor (PNET) of the cauda equina is a rare entity. 18 cases have been reported in the literature so far, including 4 cases with intracranial seeding. Moreover parenchymal involvement of brain has never been reported as a form of intracranial seeding from PNET of the cauda equina. A 31 year-old female patient, with PNET of cauda equina showing intracranial seeding 6 months after surgery, is presented in this report. To our knowledge, this is the first adult case of spinal cord PNET with parenchymal involvement of brain. The histopathological, clinical and radiological findings as well as treatment of the patient were evaluated.

摘要

马尾原始神经外胚层肿瘤（PNET）是一种罕见的疾病。迄今为止，文献中已报道18例，其中4例伴有颅内播散。此外，从未有过关于马尾PNET颅内播散形式为脑实质受累的报道。本报告介绍了一名31岁女性患者，其马尾PNET术后6个月出现颅内播散。据我们所知，这是首例脊髓PNET伴脑实质受累的成人病例。对该患者的组织病理学、临床和影像学检查结果以及治疗情况进行了评估。