García Clemente M, González Budiño T, Escobar Stein J, Seco García A J, Celorio Peinado C, Rodríguez Rodríguez J
Sección de Neumología, Hospital Alvarez-Buylla, Mieres, Asturias.
An Med Interna. 2004 Jan;21(1):27-30. doi: 10.4321/s0212-71992004000100008.
Angiosarcoma involving the lung, usually a result of metastatic disease, is a rare disorder. Primary angiosarcoma of the lung is an extremely rare tumor. The lung is one of the most common sites of metastatic involvement, along with liver and lymph nodes. Hemoptysis is the most frequent presenting symptom even with diffuse pulmonary hemorrhage. Chest radiography may reveal a spectrum of findings ranging form normal to bilateral nodular lesions. Early diagnosis is not common because of the rarity of angiosarcoma in the lung and hence, low index of suspicion. The prognosis is generally poor, with a median survival of 9 months after diagnosis.
血管肉瘤累及肺部,通常是转移性疾病的结果,是一种罕见的病症。原发性肺血管肉瘤是一种极其罕见的肿瘤。肺是转移累及最常见的部位之一,与肝脏和淋巴结一样。即使存在弥漫性肺出血,咯血仍是最常见的症状。胸部X线检查可能显示从正常到双侧结节性病变等一系列表现。由于肺血管肉瘤罕见,因此早期诊断并不常见,怀疑指数较低。总体预后较差,诊断后中位生存期为9个月。