Goodrich James Tait, Staffenberg David A
Division of Pediatric Neurological Surgery, Center for Craniofacial Disorders at the Children's Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, New York, USA.
Childs Nerv Syst. 2004 Aug;20(8-9):618-24. doi: 10.1007/s00381-004-1001-8. Epub 2004 Jun 10.
We present the case of 2-year-old craniopagus twins who are in the process of undergoing a staged separation of their craniums. In addition, they will undergo a full calvarial vault remodeling to reconstruct the lacking skull and scalp tissue in each child. We elected to do a staged separation rather than a single marathon operation for various reasons, which we will detail in this report.
The philosophy and surgical management of each step will be discussed along with the pros and cons behind the reasoning that was used. At the time of this report the children have undergone three of what are projected to be four stages of separation. Each of the stages has had unique characteristics and surgical judgments involved, and those will be reviewed.
Successful separation of viable conjoined twins has been historically a great rarity. Successful separation of twins where both have come out of surgery without any neurological deficit remains a rare occurrence and in our mind the ultimate goal.
我们介绍了一对两岁的颅联体双胞胎的病例,他们正在接受颅骨的分期分离手术。此外,他们还将接受全颅顶重塑手术,以重建每个孩子缺失的颅骨和头皮组织。出于多种原因,我们选择进行分期分离,而非单次马拉松式手术,我们将在本报告中详细说明这些原因。
将讨论每一步骤的理念和手术管理,以及所采用推理背后的利弊。在撰写本报告时,孩子们已经经历了预计四个分离阶段中的三个阶段。每个阶段都有独特的特点和涉及的手术判断,我们将对此进行回顾。
历史上,成功分离存活的联体双胞胎极为罕见。成功分离双胞胎且两人术后均无神经功能缺损仍然很少见,在我们看来,这是最终目标。