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颅缝早闭症双胞胎的术前评估:解剖学、影像学技术和手术处理。

Preoperative Evaluation of Craniopagus Twins: Anatomy, Imaging Techniques, and Surgical Management.

机构信息

From the Department of Radiology (A.E.G.-Y.), Children's Hospital of Philadelphia, Philadelphia, Pennsylvania

Departments of Radiology (A.E.G.-Y., J.M.F.).

出版信息

AJNR Am J Neuroradiol. 2020 Jun;41(6):951-959. doi: 10.3174/ajnr.A6571. Epub 2020 May 21.

Abstract

Craniopagus twins are a rare congenital malformation in which twins are conjoined at the head. Although there is high prenatal and postnatal mortality for craniopagus twins, successful separation has become more common due to advances in neuroimaging, neuroanesthesia, and neurosurgical techniques. Joined brain tissue, shared arteries and veins, and defects in the skull and dura make surgery technically challenging, and neuroimaging plays an important role in preoperative planning. Drawing on our experience from consultation for multiple successful separations of craniopagus twins, we discuss what radiologists need to know about the anatomy, classification, imaging techniques, and surgical management of craniopagus twins.

摘要

颅联胎是一种罕见的先天性畸形,双胞胎头部相连。尽管颅联胎的产前和产后死亡率很高,但由于神经影像学、神经麻醉和神经外科技 术的进步,成功分离变得更加常见。连接的脑组织、共用的动静脉以及颅骨和硬脑膜的缺陷使得手术具有挑战性,神经影像学在术前规划中发挥着重要作用。借鉴我们为多例颅联胎成功分离提供咨询的经验,我们讨论了放射科医生需要了解的颅联胎解剖、分类、成像技术和手术管理的知识。

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