Andrade M J, Canada M, Gouveia R, Carmona J, Silva A, Queiróz e Melo J, Seabra-Gomes R
Serviço de Cardiologia, Hospital de Santa Cruz, Carnaxide.
Rev Port Cardiol. 1992 May;11(5):465-70.
Anomalous origin of the left coronary artery (LCA) from the pulmonary trunk (PT) is an uncommon but frequently lethal congenital lesion of infancy. Clinically it may be difficult to distinguish from congestive cardiomyopathy, and the diagnosis is usually made by angiography. We describe the case of a 38 years old woman, in whom identification of this anomaly was achieved by 2D-Echo, pulsed Doppler and color flow mapping. She complained of fatigue, effort dyspnea and atypical chest pain. A II/VI systolic murmur at left sternal border was heard. There was cardiac enlargement on chest X-ray and ECG was suggestive of an old anterolateral myocardial infarction. The 2D-Echo study showed a dilated, poorly contracting left ventricle. A prominent right coronary ostium was recorded, but the LCA ostium could not be visualized. There was retrograde diastolic and systolic flow in proximal PT, where an anomalous vessel was seen in continuity with it by color flow mapping. Cardiac catheterization confirmed the diagnosis. The patient underwent successful reimplantation of the anomalous LCA, from the PT to the aorta. This case demonstrates usefulness of Echocardiography in the assessment of coronary artery anomalies.
左冠状动脉(LCA)起源于肺动脉干(PT)是一种罕见但在婴儿期常致命的先天性病变。临床上可能难以与充血性心肌病区分,诊断通常通过血管造影进行。我们描述了一名38岁女性的病例,通过二维超声心动图(2D-Echo)、脉冲多普勒和彩色血流图实现了对该异常的识别。她主诉疲劳、劳力性呼吸困难和非典型胸痛。在左胸骨缘可闻及II/VI级收缩期杂音。胸部X线显示心脏增大,心电图提示陈旧性前外侧心肌梗死。二维超声心动图检查显示左心室扩张、收缩功能差。记录到明显的右冠状动脉开口,但未见到LCA开口。在近端PT有舒张期和收缩期逆向血流,通过彩色血流图可见一条异常血管与其相连。心导管检查确诊。患者接受了将异常的LCA从PT重新植入主动脉的成功手术。该病例证明了超声心动图在评估冠状动脉异常中的有用性。