Benrey Jaime, Klima Tomas, Leachman Robert D., Lufschanowski Roberto
Departments of Cardiology and Pathology, St. Luke's Episcopal Hospital, Houston, Texas.
Cardiovasc Dis. 1975;2(2):205-214.
An unusual case of a middle-aged male with segmental aortitis and aortic incompetence is described. To our knowledge, only 13 cases have been previously described in the literature, but only two have had anatomopathological confirmation. Aortic incompetence is a rare manifestation of segmental aortitis. Although intrinsic abnormalities of the aortic valve have been proposed, the finding of a normal aortic valve at postmortem examination in 2 of the 3 cases in which the aortic valve was examined, supports the premise that the incompetence is probably secondary to disproportionate dilatation of the aortic root.
本文描述了一例患有节段性主动脉炎和主动脉瓣关闭不全的中年男性罕见病例。据我们所知,此前文献中仅报道过13例,但仅有两例获得了解剖病理学证实。主动脉瓣关闭不全是节段性主动脉炎的一种罕见表现。尽管有人提出主动脉瓣存在内在异常,但在3例检查了主动脉瓣的病例中,有2例在尸检时发现主动脉瓣正常,这支持了以下前提,即主动脉瓣关闭不全可能继发于主动脉根部不成比例的扩张。