Syn W-K, Ahmed M M
Gastroenterology Department, Department of Medicine, Good Hope Hospital, Birmingham, UK.
Dis Esophagus. 2004;17(2):180-2. doi: 10.1111/j.1442-2050.2004.00398.x.
Cicatricial pemphigoid is a rare, autoimmune, blistering disorder affecting the mucous membranes and skin. Esophageal involvement affects a small proportion of affected individuals and may present up to 10 years after the initial onset of the disease. We present a case of esophageal cicatricial pemphigoid that presented initially as linear IgA disease. We describe the successful treatment of dysphagia by graded esophageal dilatations.
瘢痕性类天疱疮是一种罕见的自身免疫性水疱性疾病,可累及黏膜和皮肤。食管受累在受累个体中占比小,且可能在疾病初发后长达10年才出现。我们报告一例最初表现为线状IgA病的食管瘢痕性类天疱疮病例。我们描述了通过分级食管扩张成功治疗吞咽困难的情况。