Helm T N, Bergfeld W F, Elston D
Department of Dermatology, Cleveland Clinic Foundation, Ohio.
Cutis. 1992 Sep;50(3):204-6.
Malignant angioendotheliomatosis is an angiotropic lymphoma that may present with clinical findings suggestive of thrombophlebitis or vasculitis. Examination of a biopsy specimen with special stains for leukocyte common antigen establishes the diagnosis. Although malignant angioendotheliomatosis is usually fatal, early treatment with chemotherapeutic agents is helpful. We review the characteristics and treatment of this uncommon disorder and present an illustrative case.
恶性血管内皮瘤病是一种亲血管性淋巴瘤,其临床表现可能提示血栓性静脉炎或血管炎。通过对活检标本进行白细胞共同抗原特殊染色检查可确诊。尽管恶性血管内皮瘤病通常是致命的,但早期使用化疗药物进行治疗是有帮助的。我们回顾了这种罕见疾病的特征和治疗方法,并展示了一个典型病例。