Subramaniam Kathirvel, Myers Laura B
Department of Anesthesiology and Critical Care Medicine, Beth Israel Deaconess Medical Center, Harvard Medical School, Boston, MA 02115, USA.
Paediatr Anaesth. 2004 Sep;14(9):787-91. doi: 10.1111/j.1460-9592.2004.01285.x.
Alagille syndrome (syndromic paucity of interlobular bile ducts) is the most common form of familial intrahepatic cholestasis. We describe the perioperative management of a pediatric patient with Alagille syndrome undergoing ileal exclusion and the specific issues associated with epidural anesthesia with this syndrome.
