Bartman Wojciech, Biernawska Jolanta, ŁAbuz-Roszak Beata, Kumor Klaudiusz, Pierzchała Krystyna
Katedra i Klinika Neurologii, Slaska Akademia Medyczna w Zabrzu, ul. 3 Maja 13/25, 42-800 Zabrze.
Neurol Neurochir Pol. 2004 Jul-Aug;38(4):335-9.
Certain acute anterior poliomyelitis survivors express complaints of abnormal fatigue, weakness and muscular atrophy many years after acute onset. These are basic clinical symptoms of so-called post-polio syndrome (PPS). PPS is characterized by a relatively slow, but progressive pathological muscular process, in some cases leading to functional impairment of daily living and professional activity. Breathing, speaking and swallowing impairment are common but not severe medical problems of post-polio patients. Diagnosis is usually based on a typical medical history, electromyographic investigation and exclusion of other diseases presenting similar features. We report a case of PPS in a 49-year-old woman diagnosed in the Neurological Department in Zabrze. Thirty six years after acute anterior poliomyelitis with partial recovery, new symptoms of fatigue, muscular atrophy, exertional dyspnea, walking impairment and joint pain developed. Electromyography revealed features of coexisting spinal denervation and reinnervation in tested muscles. The differential diagnosis excluded other neuromuscular diseases. The patient fulfilled clinical and electromyographic criteria of PPS.
某些急性脊髓灰质炎幸存者在急性发病多年后,会诉说有异常疲劳、虚弱和肌肉萎缩等症状。这些是所谓的小儿麻痹后遗症(PPS)的基本临床症状。PPS的特点是病理肌肉过程相对缓慢但呈进行性发展,在某些情况下会导致日常生活和职业活动的功能障碍。呼吸、说话和吞咽障碍是小儿麻痹后遗症患者常见但并不严重的医学问题。诊断通常基于典型的病史、肌电图检查以及排除其他具有相似特征的疾病。我们报告一例在扎布热神经科确诊的49岁女性小儿麻痹后遗症病例。在急性脊髓灰质炎部分恢复36年后,出现了疲劳、肌肉萎缩、劳力性呼吸困难、行走障碍和关节疼痛等新症状。肌电图显示受试肌肉存在并存的脊髓去神经和再支配特征。鉴别诊断排除了其他神经肌肉疾病。该患者符合小儿麻痹后遗症的临床和肌电图标准。