完全性房室通道合并法洛四联症伴肺动脉闭锁

Complete atrioventricular canal and tetralogy of Fallot with pulmonary atresia.

作者信息

Okamura Toru, Nagase Yuzo, Matsumoto Yasutoshi, Park In-sam, Mitsui Fujio, Shibairi Masao

机构信息

Department of Cardiovascular Surgery, Matsudo City Hospital, Chiba, Japan.

出版信息

Ann Thorac Surg. 2004 Oct;78(4):e69-71. doi: 10.1016/j.athoracsur.2003.12.056.

DOI:10.1016/j.athoracsur.2003.12.056

PMID:15464457

Abstract

Our patient was diagnosed with complete atrioventricular canal and Tetralogy of Fallot with pulmonary atresia at the age of 1 month. Then he underwent right and left Blalock-Taussig shunts at the ages of 2 months and 5 years, respectively. His cyanosis had increased at 20 years of age. Cardiac catheterization showed occlusion of the left Blalock-Taussig shunt and absence of the left pulmonary artery. Lung perfusion scintigram showed late phase perfusion in the left lung. Chest computed tomographic scan demonstrated the left pulmonary artery. We describe the operative technique of total correction.

摘要

我们的患者在1个月大时被诊断为完全性房室通道合并法洛四联症伴肺动脉闭锁。随后，他分别在2个月和5岁时接受了右、左Blalock-Taussig分流术。他在20岁时紫绀加重。心导管检查显示左Blalock-Taussig分流术闭塞，左肺动脉缺如。肺灌注闪烁扫描显示左肺晚期灌注。胸部计算机断层扫描显示了左肺动脉。我们描述了完全矫正的手术技术。