Sherif A, Stewart P, Mendes D M
Department of Surgery, St. Luke's-Roosevelt Hospital Center, New York, New York 10025.
Ann Vasc Surg. 1992 Jan;6(1):85-9. doi: 10.1007/BF02000674.
Behçet's disease is a chronic, recurrent disease that most commonly presents as oral and genital ulcers and iritis. It is a multisystem disease with possible cardiovascular, pulmonary, neurologic, cutaneous and articular involvement. It is most often diagnosed in the 20 to 40 year age group, and vascular and neurologic involvement worsens the prognosis. Vascular manifestations include venous and arterial occlusions, arterial aneurysm and pseudoaneurysm formation. We present the case of a young man with Behçet's disease with multiple aneurysms, pseudoaneurysms, arterial occlusions and venous thrombosis with a literature review. Surgeons must consider Behçet's disease when dealing with aneurysms in young patients.
白塞病是一种慢性复发性疾病,最常见的表现为口腔和生殖器溃疡以及虹膜炎。它是一种多系统疾病,可能累及心血管、肺部、神经、皮肤和关节。该病最常发生于20至40岁年龄组,血管和神经受累会使预后恶化。血管表现包括静脉和动脉闭塞、动脉动脉瘤和假性动脉瘤形成。我们报告一例患有白塞病的年轻男性病例,该患者有多个动脉瘤、假性动脉瘤、动脉闭塞和静脉血栓形成,并进行文献复习。外科医生在处理年轻患者的动脉瘤时必须考虑白塞病。