Nagayama Y, Kobayashi N, Yamabe H
Department of Medicine, Kyoto University Hospital, Japan.
Dig Dis Sci. 1992 Apr;37(4):613-7. doi: 10.1007/BF01307589.
Granuloma in the biliary system is a rare condition. The majority of the reported cases concern postsurgical granuloma. We note a patient with obstructive jaundice due to inflammatory granuloma in whom a filling defect was found at the bifurcation of the common hepatic duct by preoperative cholangiography. There have been no reported cases with similar findings. In addition to these features, this case was further characterized by consanguinity, repeated spontaneous abortions, and severe vascular lesions found in many organs that suggested the presence of a hereditary defect.
胆道系统中的肉芽肿是一种罕见病症。大多数已报道的病例为术后肉芽肿。我们注意到一名因炎性肉芽肿导致梗阻性黄疸的患者，术前胆管造影显示肝总管分叉处有充盈缺损。尚无类似发现的报道病例。除这些特征外，该病例的进一步特点是近亲结婚、反复自然流产以及在许多器官中发现严重血管病变，提示存在遗传性缺陷。
