Derrer F, Gisin S, Linka A, Kindler C H
Departement Anästhesie, Universitätsspital, Basel.
Anaesthesist. 2005 Jan;54(1):29-34. doi: 10.1007/s00101-004-0781-2.
Shone's anomaly was first described in 1963 as a developmental complex of four potentially obstructive cardiac lesions including a supravalvular fibrous mitral ring, deformity of the mitral and/or subvalvular apparatus, subvalvular aortic stenosis and coarctation of the aorta. While paediatric patients with Shone's anomaly have been reported in the literature, only a few adult patients presenting with this anomaly have been described in the perioperative period. However, patients with an undiagnosed, incomplete form of Shone's anomaly might occasionally present for non-cardiac surgery as adults. In this case report we describe the anaesthetic management of an adult patient scheduled for a non-cardiac operation, who suffered from Shone's anomaly that was unrecognised prior to the operation.
肖恩综合征于1963年首次被描述为一种由四种潜在梗阻性心脏病变组成的发育复合体,包括瓣上纤维性二尖瓣环、二尖瓣和/或瓣下装置畸形、瓣下主动脉狭窄和主动脉缩窄。虽然文献中已有小儿肖恩综合征患者的报道,但围手术期仅有少数成年肖恩综合征患者被描述。然而,患有未诊断出的、不完全形式的肖恩综合征的患者偶尔可能在成年后接受非心脏手术。在本病例报告中,我们描述了一名计划接受非心脏手术的成年患者的麻醉管理,该患者患有肖恩综合征,术前未被识别。