Nikas I, Anagnostara A, Theophanopoulou M, Stefanaki K, Michail A, Hadjigeorgi Ch
Department of Radiological Imaging, Children's Hospital Agia Sophia, Epaminonda 14, 16674, Glyfada, Athens, Greece.
Neuroradiology. 2004 Dec;46(12):1039-43. doi: 10.1007/s00234-004-1283-2. Epub 2004 Nov 18.
Desmoplastic infantile gangliogliomas (DIG) are rare intracranial tumors occurring during the 1st year of life. They arise invariably in the supratentorial region and have a great size at presentation, commonly involving more than one lobe. They are composed of a solid peripheral component of variable size, which involves the superficial cerebral cortex and the leptomeninges, and a large cystic part. Despite the great size at presentation and occasional mitotic activity in the variable undifferentiated component, this entity constitutes a distinct clinicopathological entity with benign prognosis. We hereby present the MRI and histological findings of two cases of DIG in infants aged 9 and 10 months, respectively.
促纤维增生性婴儿型节细胞胶质瘤(DIG)是发生在1岁以内的罕见颅内肿瘤。它们总是起源于幕上区域,就诊时体积很大,通常累及一个以上脑叶。它们由大小不一的实性外周成分组成,该成分累及大脑浅表皮质和软脑膜,以及一个大的囊性部分。尽管就诊时体积很大,且在可变的未分化成分中偶尔有有丝分裂活性,但该实体构成了一种具有良性预后的独特临床病理实体。我们在此分别呈现了2例年龄分别为9个月和10个月婴儿的DIG的MRI和组织学表现。